
Langerhans Cell Histiocytosis
Histiocytosis XLCH
📋Overview
Langerhans Cell Histiocytosis (LCH) is a rare disorder characterized by the abnormal proliferation of Langerhans cells, a type of dendritic cell involved in immune response. It is considered a clonal neoplastic disease with inflammatory features. LCH can affect various organs, including bone, skin, lymph nodes, lungs, and the pituitary gland. The term Langerhans Cell Histiocytosis has replaced older eponyms such as Histiocytosis X, which included subtypes like eosinophilic granuloma, Hand-Schüller-Christian disease, and Letterer-Siwe disease.
Medical codes (for reference)
UMLS CUI: C0019621ICD-10-CM
C96.6
MeSH
D006646
SNOMED CT (US)
65399007110450007
Codes are provided for reference and interoperability. They are not a diagnosis.
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