
Primary Pulmonary Hypertension
Idiopathic Pulmonary Arterial Hypertension
📋Overview
Primary Pulmonary Hypertension is a legacy term historically used to describe what is now classified as Idiopathic Pulmonary Arterial Hypertension (IPAH). It refers to high blood pressure in the pulmonary arteries without an identifiable cause. Modern terminology prefers 'Pulmonary Arterial Hypertension' (PAH), which includes idiopathic, heritable, and associated forms. This condition involves progressive narrowing and remodeling of pulmonary arteries, leading to increased resistance to blood flow and strain on the right side of the heart.
Medical codes (for reference)
UMLS CUI: C3203102ICD-10-CM
I27.0
MeSH
D065627
SNOMED CT (US)
697898008
Codes are provided for reference and interoperability. They are not a diagnosis.
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